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Table 1 Classification of systemic vasculitides according to CHCC nomenclature [3]

From: Choroidal involvement in systemic vasculitis: a systematic review

Large vessel vasculitis (LVV)
 • Takayasu arteritis (TA)
 • Giant cell arteritis (GCA)
Medium vessel vasculitis (MVV)
 • Polyarteritis nodosa (PAN)
 • Kawasaki disease (KD)
Small vessel vasculitis (SVV)
 • Antineutrophil cytoplasmic antibody (ANCA)–associated vasculitis (AAV)
  ◦ Microscopic polyangiitis (MPA)
  ◦ Granulomatosis with polyangiitis (Wegener’s) (GPA)
  ◦ Eosinophilic granulomatosis with polyangiitis (Churg-Strauss) (EGPA)
 • Immune complex SVV
  ◦ Anti–glomerular basement membrane (anti-GBM) disease
  ◦ Cryoglobulinemic vasculitis (CV)
  ◦ IgA vasculitis (Henoch-Schönlein) (IgAV)
  ◦ Hypocomplementemic urticarial vasculitis (HUV) (anti-C1q vasculitis)
Variable vessel vasculitis (VVV)
 • Behçet’s disease (BD)
 • Cogan’s syndrome (CS)
Single-organ vasculitis (SOV)
 • Cutaneous leukocytoclastic angiitis
 • Cutaneous arteritis
 • Primary central nervous system vasculitis
 • Isolated aortitis
 • Others
Vasculitis associated with systemic disease
 • Lupus vasculitis
 •Rheumatoid vasculitis
 •Sarcoid vasculitis
 • Others
Vasculitis associated with probable etiology
 • Hepatitis C virus–associated cryoglobulinemic vasculitis
 • Hepatitis B virus–associated vasculitis
 • Syphilis-associated aortitis
 •Drug-associated immune complex vasculitis
 • Drug-associated ANCA-associated vasculitis
 • Cancer-associated vasculitis
 • Others