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Table 4 Diagnostic criteria for initial onset VKH Disease

From: Clinicopathology of non-infectious choroiditis: evolution of its appraisal during the last 2–3 decades from “white dot syndromes” to precise classification

1. No ocular trauma or surgery preceding onset of disease*
2. Bilateral involvement (verified with ICGA and/or EDI-OCT) *
3. Exclusion of other infectious, inflammatory or masquerading entities, in particular other stromal choroiditis entities (i.e. tuberculosis, sarcoidosis or syphilis) *
4. Diffuse choroiditis evidenced by ICGA and/or EDI-OCT *
5. Signs and symptoms of less than 4 weeks’ duration*
6. Absence of clinical findings compatible with chronic disease (i.e. sunset glow fundus or integumentary signs (vitiligo, alopecia & poliosis) *
7. Exudative retinal detachments (evidenced by pooling and pinpoint leaking points on FA and ICGA) (very helpful criterion when present)
8. Disc hyperfluorescence (helpful criterion)
9. Neurological / auditory findings (meningismus, tinnitus, acute hearing loss) (helpful criterion)
  1. *Essential criteria