Fig. 6

Fundus color picture of a 46-year-old female with transthyretin amyloidosis. She initially was referred for blurry vision as a case of intermediate uveitis (vitritis) and retinal vasculitis in the right eye and a pars plana vitrectomy was performed in the right eye. She later presented with a left eye involvement. The pictures demonstrate retinal vascular sheathing as shown in arrows in the right eye (A) and intermediate uveitis with vitritis in the left eye (B). The genetic diagnosis of transthyretin amyloidosis was made. Fluorescein angiography showed focal vascular staining in intermediate phase (arrow) (C). The Spectral Domain OCT (SD-OCT) showed a deposit perpendicular to the retinal surface towards the vitreous from the retinal vessel (arrow) (D), and hyperfluorescent foci and staining along choroidal and retinal vessels in the supero-, infero- and temporal periphery on ICG in late phase (E)